Abstrait

Ventricular Tachicardia as a Form of Presentation of Isolated Noncompaction of Left Ventricular Myocardium

M-Jos�?�?�?�?�?�?�?© G�?�?�?�?�?�?�?©rez Callejas, Jos�?�?�?�?�?�?�?©-Tom�?�?�?�?�?�?�?¡s G�?�?�?�?�?�?�?³mez S�?�?�?�?�?�?�?¡enz, Jaione Gonz�?�?�?�?�?�?�?¡lez Aguilera, Rosario Zangr�?�?�?�?�?�?�?³niz Uru�?�?�?�?�?�?�?±uela, �?�?�?�?�?�?�?ngeles Blanco Mardones, Ana Ib�?�?�?�?�?�?�?¡�?�?�?�?�?�?�?±ez Castro and Yanett Orellana Fuentes

Isolated ventricular noncompaction left ventricular (LVNC) is a rare genetic disease characterized by left ventricular hypertrabeculation. Clinically manifested as systolic dysfunction, heart failure, ventricular arrhythmias, thromboembolic events and sudden death. It can occur alone or in combination with other congenital heart disease and / or neuromuscular disorders. It is diagnosed by echocardiography and magnetic resonance imaging and has a poor prognosis with amortality rate of 60-80%at 6 years, half of sudden death (SD). We present a case of LVNC which debuted as ventricular tachycardia.